International Journal of Clinical Pediatric Dentistry

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VOLUME 15 , ISSUE 1 ( January-February, 2022 ) > List of Articles


Amelogenesis Imperfecta and Distal Renal Tubular Acidosis: A Case Report

Nilufer Nadaf, V Krishnapriya, Arunima Chandra, G Shilpa, Santhosh K Challa, VV Ramakrishna

Keywords : Amelogenesis imperfecta, Distal renal tubular acidosis

Citation Information : Nadaf N, Krishnapriya V, Chandra A, Shilpa G, Challa SK, Ramakrishna V. Amelogenesis Imperfecta and Distal Renal Tubular Acidosis: A Case Report. Int J Clin Pediatr Dent 2022; 15 (1):121-123.

DOI: 10.5005/jp-journals-10005-2171

License: CC BY-NC 4.0

Published Online: 13-04-2022

Copyright Statement:  Copyright © 2022; The Author(s).


Amelogenesis imperfecta (AI) is an inherited dental condition affecting enamel, which can result in significant tooth discoloration and enamel breakdown, requiring lifelong dental care. Distal renal tubular acidosis (dRTA) is a condition in which the kidneys are unable to acidify the urine to a pH < 5.5 in the presence of systemic metabolic acidosis. Management of AI and dRTA patients requires both medical and dental expertise to achieve long-term successful results. The aim of this paper is to present the dental management of a child with AI and dRTA.

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