International Journal of Clinical Pediatric Dentistry

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VOLUME 8 , ISSUE 2 ( May-August, 2015 ) > List of Articles

CASE REPORT

A Rare Case Report of Neurodegenerative Disease: Duchenne Muscular Dystrophy in Two Male Siblings

B Suneja, ES Suneja, Vivek Kumar Adlakha, P Chandna

Keywords : Disorder, Hereditary, Recessive

Citation Information : Suneja B, Suneja E, Kumar Adlakha V, Chandna P. A Rare Case Report of Neurodegenerative Disease: Duchenne Muscular Dystrophy in Two Male Siblings. Int J Clin Pediatr Dent 2015; 8 (2):163-165.

DOI: 10.5005/jp-journals-10005-1306

License: CC BY-NC 4.0

Published Online: 01-08-2015

Copyright Statement:  Copyright © 2015; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Duchenne muscular dystrophy (DMD) is an recessive X-linked mediated, musculoskeletal disorder that affects only males. It is the most common and severe form of muscular dystrophy where there is failure to manufacture dystrophin. Clinically, it is characterized by progressive muscle wasting eventually leading to premature death. This case report describes the genetic, oral and systemic findings in two cases of DMD in male siblings. How to cite this article: Suneja B, Suneja ES, Adlakha VK, Chandna P. A Rare Case Report of Neurodegenerative Disease: Duchenne Muscular Dystrophy in Two Male Siblings. Int J Clin Pediatr Dent 2015;8(2):163-165.


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