International Journal of Clinical Pediatric Dentistry

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VOLUME 8 , ISSUE 3 ( September-December, 2015 ) > List of Articles

CASE REPORT

Oral Manifestations and Dental Management of Epidermolysis Bullosa Simplex

Lisa, Scheidt, Mariane Emi Sanabe, Michele Baffi Diniz

Keywords : Epidermolysis bullosa simplex, Oral manifestations, Alternative therapies

Citation Information : Scheidt L, Sanabe ME, Diniz MB. Oral Manifestations and Dental Management of Epidermolysis Bullosa Simplex. Int J Clin Pediatr Dent 2015; 8 (3):239-241.

DOI: 10.5005/jp-journals-10005-1321

License: CC BY-NC 4.0

Published Online: 00-12-2015

Copyright Statement:  Copyright © 2015; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Epidermolysis bullosa (EB) is a group of hereditary chronic disorders, characterized by fragility of the skin and mucous membranes in response to minor mechanical trauma. The objective of this study was to report the case of a young girl diagnosed with epidermolysis bullosa simplex (EBS), transmitted by an autosomal dominant gene. Cutaneous findings included blisters and dystrophy following minimal friction. Recurrent blisters and vesicle formation on the hard palate were the main oral findings. In conclusion, publications concerning the oral and clinical manifestations of EBS are important for providing knowledge and an early multidisciplinary approach that prevents blister formation and improves these patients’ quality of life, with the dentist playing an important role in oral health management. How to cite this article: Scheidt L, Sanabe ME, Diniz MB. Oral Manifestations and Dental Management of Epidermolysis Bullosa Simplex. Int J Clin Pediatr Dent 2015;8(3):239-241.


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