International Journal of Clinical Pediatric Dentistry

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VOLUME 8 , ISSUE 1 ( January-April, 2015 ) > List of Articles

CASE REPORT

Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas Revisited

KS Ravichandra, Chaitanya Ram Kandregula, Srikanth Koya, Disha Lakhotia

Keywords : Congenital insensitivity to pain and anhydrosis, Pain insensitivity, Marvan syndrome, Painless whitlows

Citation Information : Ravichandra K, Kandregula CR, Koya S, Lakhotia D. Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas Revisited. Int J Clin Pediatr Dent 2015; 8 (1):75-81.

DOI: 10.5005/jp-journals-10005-1288

License: CC BY-NC 4.0

Published Online: 01-06-2019

Copyright Statement:  Copyright © 2015; The Author(s).


Abstract

First described in 1932 by Dearborn as ‘congenital pure analgesia’, congenital insensitivity to pain and anhydrosis (CIPA) or hereditary sensory and autonomic neuropathy (HSAN) type IV is an extremely rare autosomal recessive disorder. A 7-year-old female child who is an established case of congenital insensitivity to pain and anhydrosis visited the department of pediatric medicine with osteoarthritic neuropathy. A multidisciplinary team approach was utilized to treat the child under general anesthesia. This article also discusses the diagnostic and therapeutic dilemmas involved in treating this type of children. How to cite this article: Ravichandra KS, Kandregula CR, Koya S, Lakhotia D. Congenital Insensitivity to Pain and Anhydrosis: Diagnostic and Therapeutic Dilemmas revisited. Int J Clin Pediatr Dent 2015;8(1):75-81.


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