International Journal of Clinical Pediatric Dentistry

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VOLUME 7 , ISSUE 2 ( May-August, 2014 ) > List of Articles


A Case of Dentin Dysplasia with Full Mouth Rehabilitation: A 3-year Longitudinal Study

Suneet Khandelwal, Dheeraj Gupta, Lalit Likhyani

Keywords : Dentin dysplasia, Opalescent dentin, Pulpless teeth, Radicular dentin dysplasia, Rootless teeth, Thistle tube teeth

Citation Information : Khandelwal S, Gupta D, Likhyani L. A Case of Dentin Dysplasia with Full Mouth Rehabilitation: A 3-year Longitudinal Study. Int J Clin Pediatr Dent 2014; 7 (2):119-124.

DOI: 10.5005/jp-journals-10005-1248

License: CC BY-NC 4.0

Published Online: 01-12-2017

Copyright Statement:  Copyright © 2014; The Author(s).


Dentin dysplasia, a rare hereditary disorder of dentin formation, is characterized by normal enamel but atypical dentin formation along with abnormal pulpal morphology. It is inherited as an autosomal dominant trait. It has been divided into two clinical entities: type I (radicular) and type II (coronal). Early diagnosis and initiation of effective regular dental treatments may help the patients with this condition to delay or prevent the loss of the entire dentition and help them in cope up with edentulous state in early ages. The condition undoubtedly has a negative impact on the physical and psychological well-being of the affected individual. Numerous factors have to be considered during the prosthetic rehabilitation of patients with dentin dysplasia. Treatment protocol varies according to clinical case. Although literature reports suggest general guidelines for treatment planning, the present case report describes a full mouth rehabilitation of an 8-year-old female patient with dentin dysplasia.

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