International Journal of Clinical Pediatric Dentistry

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VOLUME 6 , ISSUE 3 ( September-December, 2013 ) > List of Articles


Gorlin Syndrome with Bilateral Polydactyly: A Rare Case Report

Sonu Acharya, Swagatika Panda, Kanika Singh Dhull, Ranjan Sujit Sahoo

Keywords : Basal cell nevus syndrome, Carcinoma, Odontogenic keratocyst, Gorlin-Goltz syndrome

Citation Information : Acharya S, Panda S, Singh Dhull K, Sahoo RS. Gorlin Syndrome with Bilateral Polydactyly: A Rare Case Report. Int J Clin Pediatr Dent 2013; 6 (3):208-212.

DOI: 10.5005/jp-journals-10005-1221

License: CC BY-NC 4.0

Published Online: 01-10-2018

Copyright Statement:  Copyright © 2013; The Author(s).


Gorlin's syndrome is a rare disorder transmitted as an autosomal dominant trait. It is characterized by multiple disorders involving multiple systems. We present a case of 11-year-old male child presenting with multiple odontogenic keratocyst to the dental clinic. Retrograde diagnosis of Gorlin-Goltz syndrome was made after clinical and radiological investigation. How to cite this article: Acharya S, Panda S, Dhull KS, Sahoo SR, Ray P. Gorlin Syndrome with Bilateral Polydactyly: A Rare Case Report. Int J Clin Pediatr Dent 2013;6(3):208-212.

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