International Journal of Clinical Pediatric Dentistry

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VOLUME 6 , ISSUE 2 ( May-August, 2013 ) > List of Articles


Gorlin and Goltz Syndrome: A Case Report with Surgical Review

Rakesh N Bahadure, Eesha Surendraji Jain, Gautam P Badole

Keywords : Basal cell carcinoma, Gorlin syndrome, Nevoid basal cell carcinoma, Odontogenic keratocysts, Palmar/Plantar pits, Bifid rib, Internal strabismus

Citation Information : Bahadure RN, Surendraji Jain E, P Badole G. Gorlin and Goltz Syndrome: A Case Report with Surgical Review. Int J Clin Pediatr Dent 2013; 6 (2):104-108.

DOI: 10.5005/jp-journals-10005-1199

License: CC BY-NC 4.0

Published Online: 01-12-2017

Copyright Statement:  Copyright © 2013; The Author(s).


Gorlin and Goltz syndrome are a very complex syndrome and a multisystemic process that is characterized by the presence of multiple pigmented basocellular carcinomas, keratocysts in the jaws, palmar and/or plantar pits and calcification of the falx cerebri. Along with these major features a great number minor features have also been described which involves numerous skeletical, dermatology related, neurological, ophthalmological and reproductive anomalies. It exhibits high penetrance and variable expressivity. Presented here is the case of Gorlin-Goltz in a 12 years old male patient which was diagnosed through its oral and maxillofacial manifestations. Treatment of odontogenic keratocyst was done by enucleation without primary suturing. Iodoform dressing was kept to enhance the healing and to reduce the recurrence of the lesion. It is important to provide the early diagnosis for detection of clinical and radiological manifestations in young patients and for provision of advice concerning preventive treatment like protection of the skin from the sunlight and genetic sensitivity testing so that possible complications associated with this syndrome can be prevented. How to cite this article: Bahadure RN, Jain ES, Badole GP. Gorlin and Goltz Syndrome: A Case Report with Surgical Review. Int J Clin Pediatr Dent 2013;6(2):104-108.

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