International Journal of Clinical Pediatric Dentistry

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VOLUME 4 , ISSUE 3 ( September-December, 2011 ) > List of Articles

CASE REPORT

Oral Teratoma with a Primitive Neuroectodermal Tumor Component: A Case Report

Swetha Acharya, Amsavardani Tayaar, Sahana Adirajaiah, Gopalkrishnan Kulandswamy

Keywords : Oral teratoma, Small round cell tumor, Primitive neuroectodermal tumor, Childhood

Citation Information : Acharya S, Tayaar A, Adirajaiah S, Kulandswamy G. Oral Teratoma with a Primitive Neuroectodermal Tumor Component: A Case Report. Int J Clin Pediatr Dent 2011; 4 (3):240-243.

DOI: 10.5005/jp-journals-10005-1117

License: CC BY-NC 4.0

Published Online: 00-12-2011

Copyright Statement:  Copyright © 2011; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Teratomas are tumors of germ cell derivation consist of tissues derived from all the three germ cell layers. They comprise the most common extragonadal germ cell tumors (EGCT) in childhood. EGCTs of head and neck region account for only 5% of all benign and malignant germ cell tumors and for 6% of all teratomas. Primitive neuroectodermal tumor (PNET) arising from germ cell tumor is a distinct entity. It develops from the malignant transformation of teratomas along ectodermal lines. This paper presents a rare case of oral teratoma in a 6-year-old male who reported with pain and swelling in the right upper back teeth region of jaw. Under light microscopy, mature and immature structures representatives of trilineage derivatives were appreciated. Sheets of small round cells showing vague rosette and membranous positivity to CD-99 directed us to consider the above diagnosis.


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