Hyper IgE Disorder Associated with Multiple Fused
Primary Teeth: A Rare Clinical Occurrence

Yalamanchili Samatha; MG Manoj Kumar; Y Samata; K Srikanth Reddy

doi:10.5005/jp-journals-10005-1081i

SEARCH WITHIN CONTENT

Online First

Hyper IgE Disorder Associated with Multiple Fused Primary Teeth: A Rare Clinical Occurrence

Yalamanchili Samatha, MG Manoj Kumar, Y Samata, K Srikanth Reddy

Citation Information : Samatha Y, Manoj Kumar M, Samata Y, Srikanth Reddy K. Hyper IgE Disorder Associated with Multiple Fused Primary Teeth: A Rare Clinical Occurrence. Int J Clin Pediatr Dent 2010; 3 (3):215-218.

DOI: 10.5005/jp-journals-10005-1081i

License: CC BY-NC 4.0

Published Online: 01-06-2018

ARTICLE
REFERENCES

Abstract

The hyperimmunoglobulin E syndrome (HIES) is a multisystem disorder that affects the dentition, skeleton, connective tissues and immune system. Little is known about oral manifestations of the syndrome. The purpose of this report was to describe a 6-year-old boy with suspected autosomal recessive HIES syndrome who had multiple fused primary teeth, which is a rare association with JOB syndrome. The patient gave a history of pneumonia and skin infections. Recognition of such case at an early age is necessary to reduce morbidity. As conclusion, treatment for this condition is life long administration of therapeutic doses of penicillinase-resistant penicillin, with the addition of other antibiotics or antifungal agents as required for specific infections.

PDF Share

Sepet E, Ozdemir D, Aksakalli N, Külekçig G. Hyper-IgE syndrome: a case report. J Clin Pediatr Dent 2001;25(4): 333-336
Dental observations of hyper IgE disorder. J Clin Pediatr Dent 2007 Fall;32(1):69-72
Hyper IgE (Job’s) syndrome: A primary immune deficiency with oral manifestations. Oral Dis 2009 Jan;15(1):2-7
Severe periodontitis in a 5-year-old girl with hyperimmunoglobulin E syndrome. Pediatr Dent 2005 Jan-Feb;27(1): 68-73.

PDF Share