International Journal of Clinical Pediatric Dentistry

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VOLUME 2 , ISSUE 3 ( September-December, 2009 ) > List of Articles

CASE REPORT

Comparative Study of Dentinogenesis Imperfecta in Different Families of the Same Topographical Region

MK Jindal, Sandhya Maheshwari, Radhika Verma, Mohd Toseef Khan

Keywords : Dentin hypoplasia, shell teeth, dentinogenesis imperfecta, autosomal dominant, mesodermal defect

Citation Information : Jindal M, Maheshwari S, Verma R, Toseef Khan M. Comparative Study of Dentinogenesis Imperfecta in Different Families of the Same Topographical Region. Int J Clin Pediatr Dent 2009; 2 (3):27-34.

DOI: 10.5005/jp-journals-10005-1015

License: CC BY-NC 4.0

Published Online: 01-12-2016

Copyright Statement:  Copyright © 2009; The Author(s).


Abstract

Dental hard tissue is subject to variety of disorders. Dentinogenesis Imperfecta is one such disorder attributed to heredity. It is known to be an autosomal dominant trait. Teeth with such ‘imperfect’ dentin are liable to be weak and discolored. The disease has variable penetration and therefore can be expressed as a range of phenotypic manifestations from mild discoloration and chipping to frank attrition and multiple pulp canal exposures. Here we present a comparative study of a series of cases from different families of one topographical region with widely different presentation and histories that are characteristic of this disease.


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