International Journal of Clinical Pediatric Dentistry

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VOLUME 16 , ISSUE S1 ( August, 2023 ) > List of Articles

ORIGINAL RESEARCH

Diagnosis and Dental Management of a Child with Moebius Syndrome: A Case Report

Meenu Mittal, Radhika Chopra, Prashant Tomar

Keywords : Case report, Child, Dental management, Diagnosis, Moebius syndrome

Citation Information :

DOI: 10.5005/jp-journals-10005-2626

License: CC BY-NC 4.0

Published Online: 29-08-2023

Copyright Statement:  Copyright © 2023; The Author(s).


Abstract

Moebius syndrome (MBS) is a rare congenital nonprogressive neuromuscular disorder characterized by partial or complete, unilateral or bilateral paralysis of the facial (VII) and abducens (VI) cranial nerves (CNs). In this syndrome bilateral facial palsy may occur with the involvement of VII CN and impaired eye movements can be there because of the involvement of VI CN. It can also be associated with other CN palsies, orofacial anomalies, and limb defects. MBS is diagnosed exclusively on the basis of clinical criteria, although causative genetic patterns are being documented in recent studies. The present case report describes the dental management of a 5-year-old child diagnosed with MBS. The child presented with the abnormal shape of legs, incomplete eye closure during sleep, inability to smile, lingual hypoplasia, microstomia, and hypoplastic teeth among other dental-skeletal abnormalities, and a clinical diagnosis of MBS was made.


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