International Journal of Clinical Pediatric Dentistry

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VOLUME 14 , ISSUE 6 ( November-December, 2021 ) > List of Articles


Aberrant Location of Low-grade Myofibroblastic Sarcoma of the Gingiva in Posterior Maxilla

Neeta S Padmawar, Shivkanya Bhadange, Rachita G Mustilwar, Viddyasagar P Mopagar, Vinay H Vadvadgi, Sourabh R Joshi

Keywords : Fibroma, Gingiva, Immunohistochemistry, Maxilla, Myofibroblastic sarcoma, Posterior

Citation Information : Padmawar NS, Bhadange S, Mustilwar RG, Mopagar VP, Vadvadgi VH, Joshi SR. Aberrant Location of Low-grade Myofibroblastic Sarcoma of the Gingiva in Posterior Maxilla. Int J Clin Pediatr Dent 2021; 14 (6):816-819.

DOI: 10.5005/jp-journals-10005-2077

License: CC BY-NC 4.0

Published Online: 06-01-2021

Copyright Statement:  Copyright © 2021; The Author(s).


Low-grade myofibroblastic sarcoma is a malignant tumor arising from myofibroblasts, which has only recently become clearly defined. It represents a rare entity developing in the soft tissues of the head and neck. About 20 cases have been reported in the oral cavity, especially in the tongue and bone, while gingiva as the primary site has been described only twice to date. Diagnostic methods include histology and immunohistochemistry. The present report concerns a case of a 13-year-old female child who presented with gingival nonulcerated swelling that was interpreted for a long time as a gingival fibroma. A low-grade myofibroblastic sarcoma was diagnosed and the patient underwent a segmental osteotomy of the right posterior region of the maxilla. There was no sign of recurrence or metastatic disease during the 12-month postoperative period.

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