International Journal of Clinical Pediatric Dentistry

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VOLUME 14 , ISSUE 1 ( January-February, 2021 ) > List of Articles

CASE REPORT

Sturge–Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry

Pooja N Mapara, Swapnil M Taur, Savita G Hadakar, Shashikiran N Devendrappa, Namrata N Gaonkar, Sachin Gugawad, Dhanshri S Khade

Keywords : Computed tomography head, Dental management, GNAQ gene, Pediatric dentistry, Port-wine stains, Tranexamic acid

Citation Information : Mapara PN, Taur SM, Hadakar SG, Devendrappa SN, Gaonkar NN, Gugawad S, Khade DS. Sturge–Weber Syndrome: Roots to a Cure a Nightmare in Pediatric Dentistry. Int J Clin Pediatr Dent 2021; 14 (1):145-148.

DOI: 10.5005/jp-journals-10005-1928

License: CC BY-NC 4.0

Published Online: 14-07-2021

Copyright Statement:  Copyright © 2021; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Aim and objective: This article aims to report a case of Sturge–Weber syndrome (SWS) in a pediatric patient and its systematic dental management to add to the existing literature. Background: Sturge–Weber syndrome is one of the vascular disorders, known for its stupendous scope of clinical manifestations and life-threatening complications. The substantial prevalence of oral manifestations in SWS makes it crucial to have a comprehensive knowledge of this rare congenital disorder. Case description: This case report represents a case of SWS in an 11-year-old boy with oral, ocular, and neurological features who reported due to pain, unilateral gingival enlargement associated with spontaneous bleeding in the mandibular left region. A multidisciplinary team approach having comprehensive knowledge regarding such rare congenital disorder is a must to prevent its life-threatening complications. Conclusion: Sturge–Weber syndrome often affects the oral cavity through vascular lesions. Hence, deep knowledge is immensely important to provide an appropriate dental treatment without complications. Clinical significance: Port-wine stains should not be considered as just birthmarks and should be further investigated for its systemic involvement to arrive at a confirmatory diagnosis and treated accordingly with special precautions.


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