International Journal of Clinical Pediatric Dentistry

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VOLUME 12 , ISSUE 6 ( November-December, 2019 ) > List of Articles

CASE REPORT

Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review

Fabienne Wotjiuk, Isabelle Hyon, Sylvie Dajean-Trutaud, Zahi Badran, Tony Prud\'homme

Keywords : Dental care, Neurofibromatosis type 1, Oral manifestation

Citation Information : Wotjiuk F, Hyon I, Dajean-Trutaud S, Badran Z, Prud\'homme T. Dental Management of Neurofibromatosis Type 1: A Case Report and Literature Review. Int J Clin Pediatr Dent 2019; 12 (6):577-581.

DOI: 10.5005/jp-journals-10005-1668

License: CC BY-NC 4.0

Published Online: 01-12-2019

Copyright Statement:  Copyright © 2019; Jaypee Brothers Medical Publishers (P) Ltd.


Abstract

Neurofibromatosis type 1 (NF1) is a clinically heterogeneous neurocutaneous genetic disorder that manifests in the form of coffee-milk spots on the skin, Lish nodules, lentigines on the underarms and on the inguinal region, and neurofibromas. Orofacial manifestations of NF1 are common. Through a review of the literature, bone lesions, orthodontic and dental abnormalities, periodontal manifestations, and caries related to NF1 will be explored. In this study, we present a clinical case of a patient with neurofibroma in the oral cavity and infraocclusion of primary molars, as well as his dental management.


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