International Journal of Clinical Pediatric Dentistry

Register      Login

VOLUME 12 , ISSUE 5 ( September-October, 2019 ) > List of Articles


Management of Dentinogenesis Imperfecta: A Report of Two Cases

Avninder Kaur, Sanchit Kumar, Babita Karda, Richa Chibh

Keywords : Dentin defect, Dentinogenesis imperfecta, Shell teeth

Citation Information : Kaur A, Kumar S, Karda B, Chibh R. Management of Dentinogenesis Imperfecta: A Report of Two Cases. Int J Clin Pediatr Dent 2019; 12 (5):464-466.

DOI: 10.5005/jp-journals-10005-1681

License: CC BY-NC 4.0

Published Online: 01-10-2019

Copyright Statement:  Copyright © 2019; The Author(s).


Dentinogenesis imperfect is a hereditary dentin defect leading to discoloration as well as early tooth wear. Timely diagnosis and treatment are required to prevent further tooth loss. Two patients reported to the department of pediatrics dentistry with dentinogenesis imperfecta (DI). In the first case, patient complained of discoloration of both primary and permanent teeth and delayed eruption of permanent teeth. In the second case report, patient reported with mobile anterior tooth and missing teeth due to extraction of mobile teeth. Extraction was followed by space maintainers in the first case, and extraction was followed by partial denture in the second case. Both the patients and their parents were happy with the treatment provided.

PDF Share
  1. Kim JW, Simmer JP. Hereditary dentin defects. J Dent Res 2007;86(5):392–399. DOI: 10.1177/154405910708600502.
  2. Tahmassebi JF, Day PF, et al. Paediatric dentistry in the new millennium: dental anomalies in children. Dent Update 2003;30: 534–540. DOI: 10.12968/denu.2003.30.10.534.
  3. Witkop CJ. Genetics and dentistry. Eugen Quart 1958;5:15–21. DOI: 10.1080/19485565.1958.9987342.
  4. Holappa H, Nieminen P, et al. Splicing site mutations in dentin sialophosphoprotein causing dentinogenesis imperfecta type II. Eur J Oral Sci 2006;114:381–384. DOI: 10.1111/j.1600-0722.2006.00391.x.
  5. Shafer WG, Hine MK, et al. A textbook of Oral Pathology. 4th ed., Philadelphia: WB Saunders Co; 1983. p. 37.
  6. Review Council. Dental management of heritable dental developmental anomalies. Reference Manual 2013;39(6):348–353
  7. Kerebel B, Daculsi G, et al. Inorganic phase in dentinogenesis imperfecta. J Dent Res 1981;60:1655–1660. DOI: 10.1177/00220345810600090401.
  8. Wright JT, Gantt DG. The ultrastructure of the dental tissues in dentinogenesis imperfecta in man. Arch Oral Biol 1985;30:201–206. DOI: 10.1016/0003-9969(85)90116-5.
  9. Kamboj M, Chandra A. Dentinogenesis imperfecta type II: An affected family saga. J Oral Sci 2007;49:241–244. DOI: 10.2334/josnusd. 49.241.
  10. Guven S, Demirci F, et al. Prosthetic treatment in dentinogenesis imperfecta type II: a case report. Acta Odontol Turc 2016;33(2):86–90. DOI: 10.1111/j.1365-2842.1981.tb00481.x.
PDF Share
PDF Share

© Jaypee Brothers Medical Publishers (P) LTD.